क्या हैं हिरयामा की समस्या क्या हैं इसका इलाज जानिए एक ही वीडियो में | Hirayama Disease in hindi
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- Опубліковано 6 жов 2024
- क्या हैं हिरयामा की समस्या क्या हैं इसका इलाज जानिए एक ही वीडियो में | Hirayama Disease in hindi
Hirayama disease, also known as juvenile muscular atrophy of the distal upper extremity, is a rare neurological condition predominantly affecting young males. It is characterized by progressive muscle weakness and atrophy in the hands and forearms. Here’s a detailed overview of Hirayama disease:
Clinical Features
1. **Demographics**:
Primarily affects males aged between 15 and 25 years.
Rarely seen in females.
2. **Symptoms**:
Insidious onset of unilateral or asymmetric bilateral muscle weakness and atrophy in the forearms and hands.
Muscle fasciculations (twitches) may be present.
Cold-induced muscle cramps and weakness.
Typically, the condition progresses for a few years and then stabilizes.
3. **Distribution**:
Preferential involvement of the C7, C8, and T1 myotomes (lower cervical spinal segments).
Sparing of the proximal muscles and lower limbs.
Pathophysiology
The exact cause of Hirayama disease is not completely understood, but it is thought to be related to a dynamic compression of the cervical spinal cord during neck flexion. This leads to localized ischemia and subsequent anterior horn cell death. Key factors include:
**Flexion-induced myelopathy**: When the neck is flexed, the posterior dura mater becomes lax and can lead to anterior displacement, compressing the spinal cord.
**Ischemic changes**: Repeated and prolonged compression causes chronic ischemic changes and damage to the anterior horn cells of the spinal cord.
Diagnosis
1. **Clinical Examination**:
Detailed neurological examination focusing on muscle strength and atrophy patterns.
Observation of the neck flexion movement and associated symptoms.
2. **Imaging**:
**MRI (Magnetic Resonance Imaging)**: Key diagnostic tool. Dynamic MRI with the neck in flexion can show forward displacement of the posterior dura mater and sometimes a crescent-shaped mass compressing the spinal cord.
**Electromyography (EMG)**: Can show denervation and reinnervation in affected muscles.
Treatment
There is no cure for Hirayama disease, but treatment focuses on managing symptoms and preventing progression. Approaches include:
1. **Conservative Management**:
Use of a cervical collar to prevent neck flexion and reduce dynamic spinal cord compression.
Physiotherapy to maintain muscle strength and function.
2. **Surgical Intervention**:
Indicated in cases with significant or progressive neurological deficits despite conservative measures.
Options include anterior cervical decompression and fusion or duraplasty.
Prognosis
Hirayama disease typically has a self-limiting course, where active progression occurs over 3 to 5 years, followed by a plateau phase.
Functional prognosis is generally good, though some patients may be left with residual weakness and muscle atrophy.
Hirayama Disease
Hirayama Disease Causes
hirayama Disease Treatment
Hirayama Disease Exercise
Hirayama Disease in hindi
Hirayama Disease Detail
हीरायामा रोग
Medicines for Hirayama Diseases
हिरयामा रोग का कारण
हिरयामा रोग अनुवांशिक
हिरयामा रोग के लक्षण
हिरयामा रोग का निदान
Hand weakness
Tendon transfer
Hand not working
hand ka patla hona
Summary
Hirayama disease is a rare but distinct form of juvenile muscular atrophy affecting the distal upper limbs. Early diagnosis and management are crucial to preventing significant disability. Awareness of this condition among neurologists and orthopedic specialists can aid in timely intervention and better patient outcomes.
Praman sir ji🙏🙏❤️❤️❤️
Good
I am suffering from hiryama diseases . CMC वेल्लोर me dikhaya
To medicien diya hai
1. Neurobeanfort
2. EVION 400
Angutha aur anguli kam nhi krta thik hoga ka sir boliye
Surgery Needed
Sir mai vikas Patel up allahabad (prayagraj) se aap mera breakial flexes ka operation February me kiye the abhi result to kafi achha hai but Mera bhi hath patla ho rha hai pahle se aur abhi mere hath ki ungli me grip to bn rha hai but ungali sidha nhi kar pata to kb aau aur kya abhi thik ho sakta hai aur. Bhi
Aa sakte ho ek bar dikhane
acche se jankari dedege aapko
Sir ye problem pure tarika se khatam hoga
Thik hoga ki nhi
Sir kya aapke yanha insurance k dwara ilaaz hota h kya
Reimbursement
Sir is surgery ke complications bata dijiye plz
no complication
@@dr.amitmittalhandsurgeon6584 thank you sir
Sir 🙏 i am form odisha bhubaneswar mera bhi ei problem ho rahe 6sal hogya jada problem horahe kese treat ment ho ga sir
Bhai same .problem hai ..please share contact number
🏥 हॉस्पिटल मित्तल हैंड माइक्रो सर्जरी सेंटर जयपुर
👨⚕डॉक्टर अमित मित्तल से मिलने का समय 10 बजे से 2 बजे तक रहता है रविवार सोमवार अवकाश रहता है
जब भी आए हमे कॉल कर के अवश्य आए 📞
रविवार सोमवार अवकाश
टाइम 10 से 2 आप यहां आओगे तब टोकन मिलेगा फिर नंबर आयेगा
sunday Monday No OPD
121,122 SR Complex,Tagore Nagar,AJMER Main Road, 200 Feet Bypass Rd, Jaipur, Rajasthan 302021
ua-cam.com/video/rdmBe1AFBpc/v-deo.htmlsi=Ct1FC55n1FxEZgsi
Sir mera haath ka grip power ja chuka hai doctor bola hirayama disease ho gya hai 1.5saal hogya kaise thik hoga btaeye
Tendon transfer last options for your we will better to help you!
Tb puri tarah thik ho jayega
Sir , I was getting treatment in Bombay hospital of suspected hirayama disease , test prescribed :
Neck cervical mri (extn , fluxion) - loss of cervical lordosis detected
Blood test - vitamin d3 B 12 low , and cpkmb value was little higher
NCV and EMG- left hand was little weak .
I can share result and report .
Please advise what should I do , they are saying to go under mri again to be sure further .
It is too costly for me now.
There is no cure of this problem
Bhai sahi ho gaya hai tumara ye bimari ya nahi
@@PriyanshusinghChauhan-l8h Nhi
@@ghummakadjiggyasa7306 Mai AIIMS se chala raha hu
Thank you sir
Pahli baar koi iss topic pe koi video banaya hai mai khud ek Hirayama patient hu
तो आप ठीक हुए या नहीं
Nhi bas vitamin tablet leta hu
@@anujroyal4666aapki ko klai ki nashe fulti h kya
Kon vitamin ka@@anujroyal4666
Bhai konse vitamin lete ho batao mere bhi h esa
thanks sir mera cervical area me surgery hua tha compression roknekelia but avi v progressive hai
Sir kha karaye the aap operation
Apse contact ho skta hai Agar aap insta ya Facebook use krte hai to plz btaiye apse baat karni hai
Appko video me number de rakha hai aap diye gaye number par sampark kar sakte hain
@@anujroyal4666 Kaha se ho?
Lucknow se@@PopMemex
sir agar ye bimari h to neurosurgen se dikhana shi h ki hand surgen se ???
Hand surgeon gives you best suggestion
Sir apka youtube ka thumbnail jasa photo hai asa ho gaya hai mera 56 day ho chuka hai kiya kare sir plz reply Or ungli jam ho chuka hai kiya kare please reply 🙏
Ji agar esi samasyaho chuki hai to 6 months tak intzar kiya ja sakta hain
sir avi ungali Jaam ka Physiotherapy chal raha hai to ungli agar thik hogaya to hand vi automatic thik ho jaya ga kiya plz reply 🙏
Jay Shri Ram
Sir mere pair ke anguthe ke bagap wali ungali ka nakhu wala pura hissa kat alag ho gya tha pichle sal to kya ab wo wapas aa skti hai
Sir wrist me k wire fixation hone k 2 month bad bhi wrist me movement nhi a rha h kya ye thik ho skta h
Ji bilkul theek kiya ja sakta hai agar samay rhete iska treatment liya jaye to
Sir mujhe bhi hai kya kare
🏥 हॉस्पिटल मित्तल हैंड माइक्रो सर्जरी सेंटर जयपुर
👨⚕डॉक्टर अमित मित्तल से मिलने का समय 10 बजे से 2 बजे तक रहता है रविवार सोमवार अवकाश रहता है
जब भी आए हमे कॉल कर के अवश्य आए 📞
रविवार सोमवार अवकाश
टाइम 10 से 2 आप यहां आओगे तब टोकन मिलेगा फिर नंबर आयेगा
sunday Monday No OPD
121,122 SR Complex,Tagore Nagar,AJMER Main Road, 200 Feet Bypass Rd, Jaipur, Rajasthan 302021
ua-cam.com/video/rdmBe1AFBpc/v-deo.htmlsi=Ct1FC55n1FxEZgsi
Sir, my brother has this desease from past 5 to 6 years and his hand has became too thin the fingers are bend and are very weak. We have consulted to a lot of doctors and they each either avoid or give vitamin tablets.. i even visited the AIIMS here at rishikesh. Pls sir guide me, is there any hope to cure him or atleast recover even 20% so he can live his life.
Kindly send me your reports then after we will see and tell you!
@dr.amitmittalhandsurgeon6584 sir, i have sent the MRI report through whatsapp
How to contact sir
Check description
Hi sir me bhi hirayama disease patient hu mera grdanka opreshna karke screw wali plate lagai hei usae kuch thik nhi hora hei me aapko batana cchata hu 🙏
Ek bar beta aap api reports mujhe whatsapp par send kar dijiye
Ya ek bar aa kar dikha do!
Sir ap ka clinic hospital kahan per hai aap adress de do main aaunga
Address: 121,122 SR Complex,Tagore Nagar,AJMER Main Road, 200 Feet Bypass Rd, Jaipur, Rajasthan
Sir mera left hand patla ho raha hai please help
Aur halkapan bana raha ta hai
Lekin sir hath ma pawer hai
Please help
🏥 हॉस्पिटल मित्तल हैंड माइक्रो सर्जरी सेंटर जयपुर
👨⚕डॉक्टर अमित मित्तल से मिलने का समय 10 बजे से 2 बजे तक रहता है रविवार सोमवार अवकाश रहता है
जब भी आए हमे कॉल कर के अवश्य आए 📞
रविवार सोमवार अवकाश
टाइम 10 से 2 आप यहां आओगे तब टोकन मिलेगा फिर नंबर आयेगा
sunday Monday No OPD
121,122 SR Complex,Tagore Nagar,AJMER Main Road, 200 Feet Bypass Rd, Jaipur, Rajasthan 302021
ua-cam.com/video/rdmBe1AFBpc/v-deo.htmlsi=Ct1FC55n1FxEZgsi
Sar mera naam mahjar ali hai main up se hun mere hath mein injury Ho gai thi uska operation Ho Gaya Magar hath ki ungali Kam nahin kar rahi hath kamjor ho raha hai gadde per rahe hain yah sahi ho sakta hai
Ek bar aap apni reports bhejo\
Or sir ye disease 3 sal se hai mai apne hand se kuch kam nhi kar pata hu or mai kai hospital se treatment karwaya but hme koi relief nhi hai sir kya aap hme theek kr skte hai .
Ye disease abhi theek ho sakta hai
Bhai contact number do apna Mera v 3 ssal se h
How to contact?
6367 483221
sir mai v hiryama patient hu mujhe excercise janni hai lekin mai jharkhand se hu wha jane me bht dikkat hai aap online bta skte hai
Ji bta sakte hain
@@dr.amitmittalhandsurgeon6584 jii koi video hai aapi to uski link de dijiye ya kuch or tarika hai to batatyiye
Sir mera vi he vot jata problem he muj me vot durse hu aap se contact kse karu
Aap humare diye gaye number par sampark kar sakte hain
Sir I am a hirayama disease patient
kindly visit our clinic we will help you!
@@dr.amitmittalhandsurgeon6584
Thanks sir.
Lekin sir kya ye theek ho jayegi.
Sir Mera ulnar nerve ka operation hua hai 4 month ago abhi muze kuch result nhi hai hand mai. thumb ke portion Val musel km ho rha..
Kha se karwaya tha aapne kuch btayege aap mujhe
Nagpur se kiya tha..asha hospital mai
8 month pahile muje glass se cut laga tha elbow mai.tb se problem tha.feb mai operation kiya tha.
Sir main Assam se hu,Mera bhi brachial pluxe huyi hai 7 years ho gya tik hone ka chance hai ki nahi sir comments please 🙏🙏🙏
Yes FFMT Operation ke dwara iss chiz ka operation kiya ja sakta hain
Bhai sir ko dhka lo ok sab jaga gum lena ok Amit sir Jo result la sakte hai bo or koi nhi la sakta ok ek bar jao
Ok aap jao ek bar
Sir Hirayama disease our leprosy me Antar kaya hai 2 nishani bata dijiye sir bari meharbani hogi
Leprosy skin ki samasya hain
Hirayama Automatic hone wali motor nerve problem hain
Sir isme pure ₹ kitna lagega
Dekhne ke bad bta payege
Hello sir
My 2 hand hirayama disease 10 year
Ek bar aapko dikhane aana chahiye
Tendon transfer me kitna kharcha lagega sir btayiye please..🙏
70-80k
@@dr.amitmittalhandsurgeon6584 sir iske liye khana aana padega iska ilaaj kaha pe hoga
Hi@@dr.amitmittalhandsurgeon6584
Sir,
Kindly help same issue hein mera vi
How to talk you.
6367 483221 Send me your reports
Hii sirr
Mujhe hirayama disease hai orr bina kisi treatment ke
Meri arm ki strength pehle se kaafi increase ho gyi hai
Sir kya m apke sath call pe iss baare me discuss kr skta hoon ?
Address: 121,122 SR Complex,Tagore Nagar,AJMER Main Road, 200 Feet Bypass Rd, Jaipur, Rajasthan 302021
Kaise bhai btao ? Abhi kaise hai problem apka
@@sandeepsaha77.
@@sandeepsaha77 use nuhenz
Nurocetam +
Neurokind sachets
All 3 medicines easily available on medical store
Sir mera pAtala ho raha hai
Ek bar aa kar dikha sakte ho kya???
Hllo sir brain ka issue hai sar g grips bhut weakness h sir g please ur sujtion please 🥺🥺🥺🥺
How can I help you?
Sar meri bhi yahi samasya hai 3 salon se dheere dheere patla hota ja raha hai
Address: 121,122 SR Complex,Tagore Nagar,AJMER Main Road, 200 Feet Bypass Rd, Jaipur, Rajasthan