Von Willebrand Disease | Pathophysiology, Types, Symptoms and Treatment

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  • Опубліковано 12 гру 2024

КОМЕНТАРІ • 86

  • @zakialyamani2648
    @zakialyamani2648 5 років тому +35

    I am pretty sure VWF binds unto the GP1B, not the GPIIB/IIIa, as that is a Fibrinogen receptor.

    • @mariiakasianchyk3768
      @mariiakasianchyk3768 5 років тому +5

      Yes, you are right! It seems that this guy confuses an adhesion and aggregation.

    • @adrianpop4427
      @adrianpop4427 5 років тому +5

      Von Willebrand factor does act as bridge between platelets by binding two GP IIb/IIIa receptor on diferent platelets. Sources: ua-cam.com/video/ANXn3pUc9CA/v-deo.html, and articles www.ncbi.nlm.nih.gov/pmc/articles/PMC424474/, ashpublications.org/blood/article/105/3/1078/19658/Von-Willebrand-factor-accelerates-platelet. BUT that is aggregation, most sources agree that the platelet plug starts with adhesion which involves the platelet binding to the vWF (which is tied to collagen) via the GP Ib receptor. After that it rolls on the collagen and binds to it with GP VI and GP Ia/IIa strengthtening the bond. After this follow the GP IIb/IIIa story.

    • @shvonned.burkemsncrnpagpcn619
      @shvonned.burkemsncrnpagpcn619 4 роки тому

      Yes, I believe it can bind both domains although 1b seems to be more heavily studied.

    • @thislifeisagame9540
      @thislifeisagame9540 2 роки тому

      "VWF mediates adhesion of platelet to subendothelium by binding to platelet glycoprotein 1b, Gp2b/3a when activated and to subendothelium"
      Source -class slides

    • @abhinavmahajan3569
      @abhinavmahajan3569 2 роки тому +1

      Also missing most important concept in labs, like increased BT, PTT. Normal platelets and ristocetin test decrease agglutination.

  • @traceysmith4963
    @traceysmith4963 4 роки тому +4

    Very interesting and helpful video. I think i may have Von Willebron disease. Recently had 2 teeth extracted and ended up in the hospital due to excessive bleeding from the extraction sites. First they tried topical meds and then DDAVP. I was admitted for observation and ultimately send home later the next day. Will be following up with Hematologist.

    • @angelavrobinson4127
      @angelavrobinson4127 4 роки тому +1

      I had a similar experience. I was sent home after dentist was able to stop bleeding. Two days later I was feeling extremely fatigued went to doctor was told that I was in shock. Sent to hospital by ambulance. Received a transfusion. I had a history of dysfunctional menstrual bleeding, and nosebleeds with heavy clotting and frequent gum bleeds. I was not diagnosed until a retired army doctor referred me for testing. He had once treated a man with Von Willebrands. My fortune was being misdiagnosed with a sarcoma in my gluteus muscle. I had to return to the hematologist that had sent me to get the blood work with the National Hemophilia Foundation. I had a very expensive battery of tests was told that I had Factor VII. I was treated with Amicar. I was told sometimes stress can trigger episodes. Good Luck.

  • @McMedLife
    @McMedLife Рік тому

    Great video. Just as a quick side note in case it helps someone, Desmopressin (DDAVP) is generally *avoided* in vWD type 2B due to risk of causing thrombocytopenia (due to gain of function defect - i.e. increased affinity for platelet binding and aggregation - this is also evident in an *increased* RIPA [Ristocetin-induced platelet aggregation] at low doses, as opposed to all other types which are all typically normal or decreased).

  • @ericamaquilang9795
    @ericamaquilang9795 4 роки тому +6

    I think vWF binds to GP1b receptor of platelets

  • @dansemacabre1773
    @dansemacabre1773 4 роки тому +1

    When I was 12 they did a clotting test before I got my tonsils out. It took 25 minutes for me to stop bleeding. Tonsils weren't taken out and I got admitted to Vanderbilt's Children Hospital. I spent a month there due to the uncontrolled bleeding.

  • @aishwaryatamil8560
    @aishwaryatamil8560 Рік тому

    Very helpful video.Crisp and many concepts covered.Thank you so much

  • @DrStewartGibsonPortElizabeth
    @DrStewartGibsonPortElizabeth 4 роки тому +1

    Excellent lecture. Thanks. DDAVP is costly. Cyclokapron is effective. It is often prescribed for menorrhagia, possibly managing undiagnosed VWD, with great success.

  • @sabrinastratton1991
    @sabrinastratton1991 8 місяців тому +1

    They are testing me for it because ive had recurrent miscarriages, hemorraghed during childbirth and bled badly with dental and abdominal surgery. My menstrual cycles are awful. I do carry the Hemophilia B gene but my OB thinks VWD is the mkre likely culprit tho you can show symptoms as a hemophilia carrier.

  • @ravitejasamudrala4
    @ravitejasamudrala4 3 роки тому +1

    Hi my family history all members have Von Willebrand disease factor 8. We can take Covid-19 vaccine or not.lot of confusion please help me

  • @claudeanurudha7907
    @claudeanurudha7907 Рік тому

    Excellent presentation.Thank you so much .

  • @avishkarmaney3638
    @avishkarmaney3638 2 роки тому +2

    Vwf binds to GP1b on platelets

  • @CarlosCanepa41
    @CarlosCanepa41 3 місяці тому

    There is a chance i have this according to my doctors because my VWF is low, should i be worried? Is it deadly?

    • @competitiveconcepts7006
      @competitiveconcepts7006 3 місяці тому

      Are you fine?

    • @competitiveconcepts7006
      @competitiveconcepts7006 3 місяці тому

      What are your symptoms? Please tell me?

    • @riverogue13
      @riverogue13 2 місяці тому

      It is not deadly, and it's very easily treatable lol.

    • @CarlosCanepa41
      @CarlosCanepa41 2 місяці тому

      @riverogue13 ok thank you, the doctor said i have a minor case and it shouldnt affect me, some things are that.i cant take some medications such as aspirin, ibuprofen etc

    • @CarlosCanepa41
      @CarlosCanepa41 2 місяці тому

      @@competitiveconcepts7006 well i get frequent nosebleeds thats the main symptom

  • @picfunmedicosis1187
    @picfunmedicosis1187 3 роки тому

    Excellent sir

  • @AdyanKhan-jb1cl
    @AdyanKhan-jb1cl 11 місяців тому

    Hi sir what is the treatment of VWD my kid's have VWD kindly help me to show me the right way 🙏

  • @KimBarchok
    @KimBarchok 3 роки тому

    Thank you!

  • @barsonfamily8545
    @barsonfamily8545 5 місяців тому

    When you have VWD, can you undergo major surgery?

  • @prachiparikh8738
    @prachiparikh8738 Рік тому

    It's GP1B for vWF

  • @1Itsyasr
    @1Itsyasr Рік тому

    Great ❤!

  • @rehababdelbagi
    @rehababdelbagi 9 місяців тому

    thank u so much

  • @jafarsaif182
    @jafarsaif182 4 роки тому

    Can we give minirin tab

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    @AprilLeech-x8h 2 місяці тому

    Aylin Green

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    @WhiteheadLeona-g6e 3 місяці тому

    Clifton Road

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    @ElinorIris-v3i 2 місяці тому

    Colby Hill

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    @ShelliMarcum-v1v 2 місяці тому

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    @SharonGonzalez-c7t 3 місяці тому

    Greenfelder Cliffs

  • @zigmeebhutia2780
    @zigmeebhutia2780 3 роки тому

    Can vwd people put covid vaccine?

    • @ceecee3339
      @ceecee3339 2 роки тому

      I took it then profusely bled .. for 8 months .

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    @EdenMirabelle-v4o 2 місяці тому

    Everette Glen

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    @StephenLena-i4l 2 місяці тому

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    @CristinaStonge-v2k Місяць тому

    O'Keefe Corner

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    @BulahQuinci-p1v 3 місяці тому

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    @GraycePiersaul-b7p 2 місяці тому

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  • @samphonnetgamgee5625
    @samphonnetgamgee5625 8 місяців тому

    Wrong - VWF binds to gpIb.

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    @CarlotaSircy-z7h 2 місяці тому

    Jasper Pine

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    @марияагафоник 3 місяці тому

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    @MathildaMaxwell-q2b 3 місяці тому

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    @SonmerfieldWendell-e4q 2 місяці тому

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  • @MK-bi8xl
    @MK-bi8xl 10 місяців тому +1

    its gp1b complex for vwf !!!!!

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    @TolandVicky-w7y 3 місяці тому

    Stark Motorway

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    @LuciusIngemar-b1v 2 місяці тому

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    @MaryHinkson-s4j 2 місяці тому

    Bert Views

  • @PADMAVATHISURA
    @PADMAVATHISURA 7 місяців тому

    Thank you 💕

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    @dimakim-n6c 3 місяці тому

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